庫存單位: E-AB-53557_120μL-ES

WDSUB1多株抗體,120 μL

WDSUB1(WD 重複、SAM 和 U-box 結構域含蛋白 1),也稱為 UBOX6 或 WDSAM1,是一種 476 個胺基酸的蛋白質,含有一個 SAM(不孕 alpha 基序)結構域、一個 U-box 結構域和七個 WD 重複序列。 WDSUB1 由於可變剪接而以兩種亞型存在,由位於 2 號染色體上的基因編碼。 2 號染色體是人類第二大染色體,編碼超過 1,400 個基因,佔人類基因組的近 8%,包含許多與疾病相關的基因。彩色魚鱗病是一種罕見且病態的皮膚畸形,與 ABCA12 基因突變有關,而脂質代謝紊亂谷甾醇血症與 ABCG5 和 ABCG8 基因缺陷有關。此外,一種極為罕見的隱性遺傳疾病——Alstrm 綜合徵,是由位於 2 號染色體的 ALMS1 基因突變引起的。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.7 毫克/毫升

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Calculated Molecular Weight:53千道爾頓

Observed Molecular Weight:參考圖

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:53千道爾頓

Dilution:寬螢幕 1:500-1:2000

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Application:世界銀行

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Research Areas:細胞生物學

Species Reactivity:人;小鼠

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Conjugation:未結合

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