庫存單位: E-AB-53204_200μL-ES

VMA21多株抗體,200 μL

此基因編碼溶小體液泡 ATPase 組裝的伴侶分子。內質網中液泡 ATPase (V-ATPase) 的 V0 複合物組裝所需。與液泡 ATPase(V-ATPase)的 V0 複合物相關。 MEAX 是一種兒童期發病的疾病,其特徵是骨骼肌逐漸空泡化和萎縮。此病以隱性方式遺傳,影響男孩,而不影響帶因者女性。此病在兒童時期發病,患者表現為下肢近端肌肉無力,隨著時間的推移逐漸進展至其他骨骼肌群。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:150-1:500;免疫螢光 1:50-1:200

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Application:免疫組化;

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Research Areas:細胞生物學;訊號傳導

Species Reactivity:人;小鼠

Reactivity:

Target Synonym:VMA21;液泡 ATPase 組裝因子;過度自噬性肌病變蛋白;MEAX;XMEA;液泡 ATPase 組裝整體膜蛋白 VMA21;VMA21 液泡 H+-ATPase 同源物 (S. Cerevisiae);過度自噬性肌肉病變;VMA21 液泡 H+-ATPase 同源物。

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Conjugation:未結合

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