庫存單位: E-AB-22144_60μL-ES

TTR單株抗體,60 μL

此基因編碼轉甲狀腺素蛋白,它是三種前白蛋白之一,包括α-1-抗胰蛋白酶、轉甲狀腺素蛋白和血清類黏蛋白。轉甲狀腺素蛋白是一種載體蛋白;它運送血漿和腦脊髓液中的甲狀腺激素,也運送血漿中的視黃醇(維生素A)。該蛋白質由相同亞基的四聚體組成。據報道,該基因有 80 多種不同的突變;大多數突變與澱粉樣蛋白沉積有關,主要影響週邊神經和/或心臟,一小部分基因突變是非澱粉樣變性的。突變引起的疾病包括澱粉樣多發性神經病變、甲狀腺功能正常的高甲狀腺素血症、澱粉樣玻璃體混濁、心肌病變、眼腦膜澱粉樣變性、腦膜腦血管澱粉樣變性、腕管綜合症等。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:1毫克/毫升

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Observed Molecular Weight:16kDa

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫印跡 1:500-2000

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Application:WB;IHC-p

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Research Areas:癌症;心血管;神經科學

Species Reactivity:人類

Reactivity:

Target Synonym:澱粉樣多發性神經病變;澱粉樣變性 I;ATTR;腕管綜合症 1;CTS;CTS1;異常白蛋白血症性甲狀腺機能性高甲狀腺素血症;異常轉甲狀腺素血症性高甲狀腺素血症;附睾腔內蛋白 111;HEL111;HsT2651;PALB2CCHHII) 前澱粉樣澱粉樣蛋白; ;TTR;TTR 蛋白

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Buffer:含有 0.02% 疊氮化鈉和 50% 甘油的 PBS,pH 值為 7.4。

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Conjugation:未結合

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