庫存單位: E-AB-18755_20μL-ES

TIMM8A 多克隆抗體,20 μL

此轉位酶參與疏水性膜蛋白從細胞質進入和插入粒線體內膜。該基因在 Mohr-Tranebjaerg 症候群/耳聾肌張力失調症候群 (MTS/DDS) 中發生突變,推測 MTS/DDS 是由於粒線體蛋白質輸入系統缺陷導致的粒線體疾病。此基因缺陷也會導致詹森症候群;一種伴隨視聽神經萎縮和肌肉無力的 X 連鎖疾病。此蛋白質與 TIMM13 一起形成 70 kDa 異六聚體。可變剪接產生編碼不同亞型的多個轉錄變異。

定價
$105.12 USD
售價
$105.12 USD
定價
2-4週
Hassle-Free Warranty
Safe & Secure Payment
Livetime Tech Support
  • Specification
  • Downloads
  • Reviews
$105.12
ADD TO CART
ADD TO CART

Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

Warranty:

Safety Performance:

Protection Class:

Sterile Status:

Reconstitution:

Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

Battery:

Battery Service Life:

Component:

Technical Specifications

Capacity:

Concentration:0.84 毫克/毫升

Dimension [D×W×H]:

Diameter:

Length:

Width:

High:

Volume:

Volume Range:

Speed:

Speed Range:

Max.Speed:

Max. RCF:

Temperature Range:

Operating Temperature Range:

Permissible Ambient Temperature :

Permissible Relative Humidity:

Input voltage:

Power Requirements:

Voltage/Frequency:

Sensitivity:

Specificity:

Precision:

Speed Accuracy:

Volume Accuracy:

Particle Size:

Pore Size:

Binding Capacity:

Calculated Molecular Weight:

Observed Molecular Weight:

Purity:

Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

Random Error:

Acceleration/Braking time:

Aspiration Speed:

Calculated Molecular Weight:

Dilution:免疫組化 1:40-1:200

Driving Motor DC motor:

Em:

Ex:

Endotoxin:

Flow rate [liquid]:

Features and Capabilities

Application:免疫組織化學

Detection Target:

Detection Type:

Detection Range:

Research Areas:神經科學;訊號傳導

Species Reactivity:人類;小鼠;大鼠

Reactivity:

Target Synonym:DDP 1;順鉑; DDP1;耳聾肌張力障礙蛋白1;耳聾/肌張力障礙肽; DFN 1; DFN1; MGC12262;線粒體進口內膜轉位酶亞基Tim8A;多學科測試系統;蒂姆 8A;定時8;蒂姆8A;蒂姆8A; TIMM 8A; timm8a;線粒體內膜轉位酶8同源物A; X連鎖耳聾肌張力障礙蛋白; X連鎖耳聾肌張力障礙蛋白

Test Principle:

Quantitative/Qualitative :

Result Type:

Materials :

Assay Time:

Autoclave component:

Available Rotor Adapters:

Binding Capacity:

Bio-activity:

Bottom Shape:

Bottom Type:

Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

Cap Color:

Clonality:多克隆

Conjugation:未結合

Coupled Ligand:

Cover Type:

Detection Instrument :

Dispensing Speed:

Display:

Form:

Formulation:

Graduation:

Growth Area:

Download File