庫存單位: PKSH032894_10μg-ES

重組人 PMM2 蛋白 (His 標籤), 10 μg

磷酸甘露糖變位酶 2 (PMM2) 是一種酶,屬於高度可變的甲基轉移酶超家族的成員。 PMM2 是一種細胞質蛋白,能催化甘露糖 6-磷酸異構化為甘露糖 1-磷酸。此外,PMM2 也參與了許多關鍵甘露糖基轉移反應所需的 GDP-甘露糖和多萜醇-磷酸-甘露糖的合成。 PMM2 缺陷可導致先天性糖基化障礙 1A 型 (CDG1A)。先天性糖基化障礙是糖蛋白生物合成的代謝缺陷,通常會導致嚴重的智力和精神運動障礙。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Sterile Status:

Reconstitution:不適用

Shipping:本產品以液體形式提供。它是在冷凍溫度下用藍冰/凝膠包運輸的。收到後,立即存放在<-20°C的環境中。

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Calculated Molecular Weight:29.1 kDa

Observed Molecular Weight:29千道爾頓

Purity: 以還原 SDS-PAGE 測定,結果 > 95%。

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Storage:儲存溫度<-20°C,可穩定保存6個月。請盡量減少凍融循環。

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Calculated Molecular Weight:29.1 kDa

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Endotoxin: 經 LAL 方法測定,每 μg 蛋白質含量 < 1.0 EU。

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Bio-activity:未驗證活動

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Formulation:以 20mM Tris-HCl、150mM NaCl、pH 8.0 的 0.2 μm 過濾溶液形式提供。

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