庫存單位: PKSH032032_10μg-ES

重組人 ACADM/MCAD 蛋白 (His 標籤), 10 μg

中鏈特異性醯基輔酶 A 脫氫酶 (ACADM) 是一種粒線體脂肪酸 β-氧化,屬於醯基輔酶 A 脫氫酶家族。 ACADM 是一種同型四聚體酶,可催化粒線體脂肪酸 β-氧化途徑的初始步驟。 ACADM 專門針對醯基鍊長度為 4 至 16 的物質。它對於將這些特定的脂肪酸轉化為能量至關重要,尤其是在禁食期間。 ACADM 缺陷會導致中鏈醯基輔酶 A 去氫酶缺乏症,這種疾病的特徵是肝功能障礙、空腹低血糖和腦病,可能導致嬰兒死亡。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Reconstitution:不適用

Shipping:本產品以液體形式提供。它是在冷凍溫度下用藍冰/凝膠包運輸的。收到後,立即存放在<-20°C的環境中。

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Calculated Molecular Weight:45.9 kDa

Observed Molecular Weight:42千道爾頓

Purity: 以還原 SDS-PAGE 測定,結果 > 95%。

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Storage:儲存溫度<-20°C,可穩定保存6個月。請盡量減少凍融循環。

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Calculated Molecular Weight:45.9 kDa

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Endotoxin: 經 LAL 方法測定,每 μg 蛋白質含量 < 1.0 EU。

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Research Areas:訊號傳導;心血管;癌症;代謝;

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Bio-activity:未驗證活動

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Formulation:以 20mM 醋酸鹽、10% 海藻糖、0.05% Tween 80、pH 5.0 的 0.2 μm 過濾溶液形式提供。

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