庫存單位: E-AB-52713_60μL-ES

QDPR多株抗體,60 μL

此基因編碼二氫蝶呤還原酶,可催化 NADH 介導的醌類二氫生物蝶呤還原。此酵素是蝶呤依賴性芳香族胺基酸羥基化系統的重要組成部分。導致 QDPR 缺乏的該基因突變包括異常剪接、胺基酸替換、插入或過早終止。二氫蝶呤還原酶缺乏症因苯丙胺酸羥化酶的輔因子生物蝶呤產生不足而表現為非典型苯酮尿症。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Calculated Molecular Weight:26千道爾頓

Observed Molecular Weight:參考圖

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:26千道爾頓

Dilution:免疫印跡法 1:500-1:2000

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Application:免疫組化

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Research Areas:代謝;訊號傳導

Species Reactivity:人類;小鼠;大鼠

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Target Synonym:6;7 二氫蝶啶還原酶;DHPR;DHPR;二氫蝶啶還原酶;HDHPR;HPR;PKU2;Qdpr;醌二氫蝶啶還原酶;SDR33C1;短鏈去氫酶/還原酶家族 33C;成員 1

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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