庫存單位: E-AB-13533_20μL-ES

PPOX多株抗體,20 μL

此基因編碼血紅素生物合成的倒數第二個酶,該酶催化原卟啉原 IX 的 6 電子氧化形成原卟啉 IX。此基因突變會導致混合型卟啉症,這是一種常染色體顯性血紅素代謝障礙,因位於內線粒體膜上的酶原卟啉原氧化酶缺乏而引起。編碼相同蛋白質的剪接轉錄變異體已被鑑定。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.4 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:50-1:200

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Application:免疫組織化學

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Research Areas:癌症;代謝;標籤和細胞標記

Species Reactivity:人;小鼠

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Target Synonym:MGC8485;PPO;PPOX;PPOX;原卟啉原氧化酶;V290M;多變性卟啉症;VP

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Clonality:多克隆

Conjugation:未結合

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