庫存單位: E-AB-19756_200μL-ES

NOG多株抗體,200 μL

NOG(Noggin)是一種蛋白質編碼基因。與 NOG 相關的疾病包括跗骨腕骨聯合症候群和 B2 型短指症。其相關途徑包括中胚層承諾途徑及分化途徑。與此基因相關的 GO 註釋包括蛋白質同型二聚化活性和細胞激素結合。此基因編碼的分泌多肽可結合併滅活轉化生長因子-β(TGF-β)超家族訊號蛋白的成員,例如骨形態發生蛋白 4(BMP4)。該蛋白質似乎具有多效性,無論是在發育早期還是在後期。它最初是從非洲爪蟾中分離出來的,因為它能夠恢復經紫外線處理人工腹化的胚胎的正常背腹體軸。小鼠直系同源物的敲除結果顯示它參與了許多發育過程,例如神經管融合和關節形成。最近,在患有近端指骨聯合綜合徵(SYM1)和多發性骨性縫合綜合徵(SYNS1)的無關家族中發現了幾種顯性人類 NOG 突變; SYM1 和 SYNS1 都以多關節融合為主要特徵,並且與此基因映射到同一區域(17q22)。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:1.4 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:30-1:150

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Application:免疫組織化學

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Research Areas:癌症;發育生物學;幹細胞

Species Reactivity:人;小鼠

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Target Synonym:木栓;諾格;頭;標準 1;SYM1;指關節合併 1 (近端);骨性縫合(多發性)症候群 1;同步 1;SYNS1

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Clonality:多克隆

Conjugation:未結合

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