庫存單位: E-AB-18659_60μL-ES

MYOZ2多株抗體,60 μL

MYOZ2(Myozenin 2)是一種蛋白質編碼基因。與 MYOZ2 相關的疾病包括肥厚性心肌病變、16 和 Myoz2 相關家族性肥厚性心肌病變。與此基因相關的 GO 註釋包括肌動蛋白結合和 telethonin 結合。該基因的一個重要旁系同源物是MYOZ1。此基因編碼的蛋白質屬於與鈣調神經磷酸酶結合的肌節蛋白家族,鈣調神經磷酸酶是一種參與多種細胞類型中鈣依賴性訊號傳導的磷酸酶。這些家族成員將鈣調神經磷酸酶與心肌和骨骼肌細胞肌節 z 線上的 α-輔肌動蛋白連接起來,因此它們對於鈣調神經磷酸酶訊號傳導很重要。此基因突變會導致家族性肥厚型心肌病變 16 型,這是一種遺傳性心臟病。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:1.32 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:40-1:200

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Application:免疫組織化學

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Research Areas:心血管;訊號傳導

Species Reactivity:人;小鼠

Reactivity:

Target Synonym:C4orf5;鈣調神經磷酸酶結合蛋白鈣調素1;鈣調素 1;鈣調素-1;鈣調素1; CMH16; CS 1; CS1;FATZ相關蛋白2;FATZ相關蛋白2;肌肉特異性蛋白質;MYOZ 2; MYOZ2;MYOZ2;肌肽-2;肌肽-2;肌肽2;

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Clonality:多克隆

Conjugation:未結合

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