{"product_id":"mvk-polyclonal-antibody-20-μl","title":"MVK多株抗體，20 μL","description":"\u003cp\u003e \n此基因編碼過氧化物酶體酶甲羥戊酸激酶。甲羥戊酸是異戊二烯和甾醇合成中的關鍵中間體，甲羥戊酸激酶是異戊二烯和甾醇合成中的關鍵早期酵素。此基因突變引起的甲羥戊酸激酶缺乏症會造成甲羥戊酸尿症，這種疾病的特徵是精神運動遲緩、發育不良、肝脾腫大、貧血和反覆發熱危象。此基因缺陷還會導致高免疫球蛋白血症 D 和週期性發燒綜合徵，該綜合徵的特徵是反覆發熱，並伴有淋巴結腫大、關節痛、胃腸道不適和皮疹。\n\u003c\/p\u003e\n\n","brand":"Elabscience","offers":[{"title":"Default Title","offer_id":47121295737056,"sku":"E-AB-11414_20μL-ES","price":87.6,"currency_code":"USD","in_stock":true}],"url":"https:\/\/apac.labcart.com\/zh\/products\/mvk-polyclonal-antibody-20-%ce%bcl","provider":"LabCart Life Science-APAC","version":"1.0","type":"link"}