{"product_id":"idua-polyclonal-antibody-20-μl","title":"IDUA 多株抗體，20 μL","description":"\u003cp\u003e \n此基因編碼一種酶，可水解兩種糖胺聚醣（硫酸皮膚素和硫酸肝素）的末端 α-L-艾杜醣醛酸殘基。這種水解是這些糖胺聚醣的溶酶體降解所必需的。此基因突變會導致酵素缺乏，從而引發常染色體隱性遺傳疾病黏多醣貯積症 I 型 (MPS I)。\n\u003c\/p\u003e\n\n","brand":"Elabscience","offers":[{"title":"Default Title","offer_id":47119595077856,"sku":"E-AB-18101_20μL-ES","price":87.6,"currency_code":"USD","in_stock":true}],"url":"https:\/\/apac.labcart.com\/zh\/products\/idua-polyclonal-antibody-20-%ce%bcl","provider":"LabCart Life Science-APAC","version":"1.0","type":"link"}