{"product_id":"ids-polyclonal-antibody-60-μl-1","title":"IDS多株抗體，60 μL","description":"\u003cp\u003e\n艾杜醣醛酸 2-硫酸酯酶 (IDS) 是溶小體降解硫酸乙醯肝素和硫酸皮膚素所必需的。導致人類IDS缺乏的突變，會造成這些醣胺聚醣在溶小體中儲存，進而引發亨特氏症候群（一種X染色體連鎖疾病）。發生內部蛋白水解裂解，產生存在於人類肝臟中的成熟IDS，其顯示含有42 kDa多肽的N末端至14 kDa多肽。\n\u003c\/p\u003e\n\n","brand":"Elabscience","offers":[{"title":"Default Title","offer_id":47118301790432,"sku":"E-AB-53138_60μL-ES","price":171.6,"currency_code":"USD","in_stock":true}],"url":"https:\/\/apac.labcart.com\/zh\/products\/ids-polyclonal-antibody-60-%ce%bcl-1","provider":"LabCart Life Science-APAC","version":"1.0","type":"link"}