庫存單位: E-AB-18691_20μL-ES

HMBS多株抗體,20 μL

此基因編碼羥甲基膽烷合成酶超家族的一個成員。編碼的蛋白質是血紅素生物合成途徑的第三種酶,催化四個膽色素原分子從頭到尾合成線性羥甲基膽烷。此基因的突變與體染色體顯性遺傳疾病急性間歇性卟啉症有關。已經描述了編碼不同異構體的剪接轉錄變體。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:1.08 毫克/毫升

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Calculated Molecular Weight:39千道爾頓

Observed Molecular Weight:參考圖

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:39千道爾頓

Dilution:寬螢幕 1:500-1:2000

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Features and Capabilities

Application:世界銀行

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Research Areas:癌症;細胞生物學;代謝;訊號傳導

Species Reactivity:人類;小鼠;大鼠

Reactivity:

Target Synonym:HEM3;甲基安息香酸;羥甲基膽烷合酶; PBG D; PBG-D; PBGD;前次發病率;膽色素原脫氨酶;卟啉症;急性;切斯特型;前尿卟啉原合酶;前尿卟啉原合酶; UPS;尿卟啉原 I 合酶;尿卟啉原I合成酶

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Clonality:多克隆

Conjugation:未結合

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