庫存單位: E-AB-19032_200μL-ES

GATM多株抗體,200μL

此基因編碼屬於脒基轉移酶家族的粒線體酶。這種酵素參與肌酸的生物合成,透過催化胍基從 L-精氨酸轉移到甘氨酸,產生胍基乙酸,即肌酸的直接前驅物。此基因突變會導致精胺酸:甘胺酸脒基轉移酶缺乏症,這是一種先天性肌酸合成缺陷,其特徵是認知障礙、語言障礙和行為障礙。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:1.26 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:50-1:300

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Application:免疫組織化學

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Research Areas:癌症;代謝;訊號傳導

Species Reactivity:人類;小鼠;大鼠

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Target Synonym:阿加特;在;關貿總協定;關貿總協定;甘氨酸脒基轉移酶;甘氨酸脒基轉移酶;粒線體; L-精氨酸:甘氨酸脒基轉移酶;粒線體;轉氨酶

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Clonality:多克隆

Conjugation:未結合

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