庫存單位: E-AB-52080_20μL-ES

G6PC多株抗體,20 μL

葡萄糖-6-磷酸酶 (G6Pase) 是內質網的多亞基整合膜蛋白,由催化亞基和 G6P、無機磷酸鹽和葡萄糖的轉運蛋白組成。此基因(G6PC)是人類三個葡萄糖-6-磷酸酶催化亞基編碼基因之一:G6PC、G6PC2 和 G6PC3。葡萄糖-6-磷酸酶催化 D-葡萄糖 6-磷酸水解為 D-葡萄糖和正磷酸鹽,是葡萄糖穩態中的關鍵酶,在糖質新生和肝醣分解中發揮作用。此基因突變會導致 I 型肝醣累積病 (GSD1)。這種疾病也稱為馮吉爾克病,是一種代謝紊亂症,其特徵是嚴重的低血糖,並伴隨肝臟和腎臟中肝醣和脂肪的積聚。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:70-1:350

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Application:免疫組織化學

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Research Areas:癌症;細胞生物學;代謝

Species Reactivity:人類;小鼠;大鼠

Reactivity:

Target Synonym:AW107337;G-6-Pase;G6Pase;G6Pase-alpha;g6pc;G6PC;G6PT;葡萄糖-6-磷酸酶alpha;葡萄糖-6-磷酸酶;GSD1;GSD1a;MGC163350;MGC93613;RP23-281CRP23-281C18.

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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