庫存單位: AN000510P_25μg-ES

Frataxin/FXN 多株抗體,25 μg

FXN,又稱FRDA、X25、m81-FXN、d-FXN、m78-FXN和i-FXN,屬於frataxin家族。它透過將 Fe2+ 輸送到參與這些途徑的蛋白質來促進血紅素的生物合成以及鐵硫簇的組裝和修復。 FXN 可能透過催化 Fe2+ 氧化為 Fe3+ 的能力在抵抗鐵催化的氧化壓力中發揮作用;寡聚形式具有體外亞鐵氧化酶活性,但單體形式不具有。 FXN 被切割成 4 條鏈。 FXN 在細胞質中以 210 個氨基酸 (AA) 前體蛋白 (pFXN;23?KDa) 的形式表達,該蛋白被轉位到線粒體中,在那裡經過兩個連續步驟加工成 iFXN (FXN 42-210;19?KDa) 並最終形成具有功能的 mFXN (81-210K;Da1K?DaK?)。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:1毫克/毫升

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Shelf Life:12個月

Storage:4°C 下儲存有效期限為 12 個月,-20°C 下儲存有效期限為長期儲存,避免凍融循環。

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Dilution:ELISA 捕捉 2-8 μg/mL;ELISA 檢測 0.1-0.4 μg/mL

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Application:ELISA 擷取/檢測儀

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Research Areas:癌症;代謝;訊號傳導;標籤和細胞標記

Species Reactivity:人類

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Target Synonym:CyaY;d-FXN;FA;FARR;Frataxin 成熟形式;Frataxin(81-210);FRDA;FRDA;Friedreich 共濟失調蛋白;Fxn;i-FXN;m56-FXN;m78-FXN;m81-FXN;MGC57199;X2557199;X2557199;X2557199;X2557199;X2557199;X2557199;

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Buffer:磷酸鹽緩衝溶液,pH 值為 7.2,含 0.05% proclin 300。

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Clonality:多克隆

Conjugation:未結合

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