庫存單位: E-AB-11240_120μL-ES

FLNA多株抗體,120 μL

此基因編碼的蛋白質是一種肌動蛋白結合蛋白,可交聯肌動蛋白絲並將肌動蛋白絲與膜糖蛋白連接起來。編碼的蛋白質參與重塑細胞骨架以影響細胞形狀和遷移的變化。此蛋白質與整合素、跨膜受體複合物和第二信使相互作用。此基因缺陷是多種症候群的原因,包括腦室周圍結節性異位症(PVNH1、PVNH4)、耳顎指症候群(OPD1、OPD2)、額骨骺發育不良(FMD)、梅爾尼克-尼德爾斯症候群(MNS)和X連鎖先天性特發性腸假性阻塞(CIIPX)。已發現該基因有兩種編碼不同異構體的轉錄變異。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.6 毫克/毫升

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Calculated Molecular Weight:281kDa

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:281kDa

Dilution:免疫印跡法 1:500-1:2000

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Features and Capabilities

Application:免疫組化

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Research Areas:癌症;訊號傳導

Species Reactivity:人;小鼠

Reactivity:

Target Synonym:ABP 280;ABP-280;肌動蛋白結合蛋白 280;α 細絲蛋白;α-細絲蛋白;APBX;CSBS;CVD1;內皮肌動蛋白結合蛋白;內皮肌動蛋白結合蛋白;細絲蛋白 1;細絲蛋白 AABPNFLNMAMUSFilav-1;FFLNMATRTTMCSSMCSSMCS4MCS4MCS4MCS4MMCS4MMCS4MMCS4MMr;FelAA4MA4MAAT等待AT等待A等待早期纖維蛋白蛋白A管理基因; ;非肌肉纖維蛋白;OPD;OPD1;OPD2;XLVD;XMVD

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Clonality:多克隆

Conjugation:未結合

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