庫存單位: E-AB-19886_200μL-ES

FKTN多株抗體,200 μL

此基因編碼的蛋白質是一種假定的跨膜蛋白,位於順式高爾基體區室,可能參與骨骼肌中 α-肌肉營養不良症聚醣的糖基化。編碼的蛋白質被認為是一種糖基轉移酶,可能在大腦發育中發揮作用。此基因缺陷是導致福山型先天性肌肉營養不良症 (FCMD)、沃克-華伯格症候群 (WWS)、2M 型肢帶型肌肉失養症 (LGMD2M) 和 1X 型擴張型心肌病變 (CMD1X) 的原因。已發現該基因的剪接轉錄變異體。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:1.08 毫克/毫升

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Calculated Molecular Weight:54千道爾頓

Observed Molecular Weight:參考圖

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:54千道爾頓

Dilution:寬螢幕 1:500-1:2000

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Features and Capabilities

Application:世界銀行

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Research Areas:癌症;發育生物學;標籤和細胞標記

Species Reactivity:人;小鼠

Reactivity:

Target Synonym:命令1X; FCMD;FCMD基因;FKTN; FKTN;福田;福山型先天性肌肉營養不良蛋白;福山型先天性肌肉營養不良蛋白;LGMD2M;MDDGA4; MDDGB4; MDDDGC4;MGC126857;

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Clonality:多克隆

Conjugation:未結合

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