庫存單位: E-AB-10320_20μL-ES

FGFR1多株抗體,20 μL

此基因編碼的蛋白質是成纖維細胞生長因子受體(FGFR)家族的成員,該家族的氨基酸序列在成員之間以及整個進化過程中高度保守。 FGFR 家族成員在配體親和力和組織分佈方面彼此不同。全長代表性蛋白質由一個細胞外區域組成,該區域由三個免疫球蛋白樣結構域、一個疏水跨膜片段和一個細胞質酪胺酸激酶結構域組成。蛋白質的細胞外部分與纖維母細胞生長因子相互作用,引發一系列下游訊號,最終影響有絲分裂發生和分化。這個特定的家族成員結合酸性和鹼性成纖維細胞生長因子並參與肢體誘導。此基因突變與 Pfeiffer 症候群、Jackson-Weiss 症候群、Antley-Bixler 症候群、骨質疏鬆症和常染色體顯性 Kallmann 症候群 2 有關。涉及該基因的染色體畸變與幹細胞骨髓增生性疾病和幹細胞白血病淋巴瘤症候群有關。已經描述了編碼不同蛋白質亞型的剪接變體;但並非所有變體都已充分錶徵。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.6 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:50-1:300

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Application:免疫組織化學

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Research Areas:癌症;心血管;表觀遺傳學和核子訊號;神經科學;訊號傳導

Species Reactivity:人類;小鼠;大鼠

Reactivity:

Target Synonym:鹼性纖維母細胞生長因子受體 1;bFGF-R-1;BFGFR;CD331;CEK;FGFBR;FGFR 1;FGFR-1;FGFR1;FGFR1/PLAG1 融合;FGFR1;纖維母細胞生長因子受體 1;FLG;FLT-2;FLT2;FGFR1;纖維母細胞生長因子受體 1;FLG;FLT-2;FLT2;Fms HHH2;FmsHHHDS 類激酶生長; ;羥芳基蛋白激酶;KAL2;N-SAM;OGD;原癌基因 c-Fgr

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Conjugation:未結合

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