庫存單位: AN00298L_100μL-ES

Elab Fluor® 488 結合層蛋白 A/C 單株抗體,100 μL

層蛋白A/C也被命名為LMNA或LMN1。層蛋白家族構成基質並且在演化過程中高度保守。在有絲分裂過程中,由於層蛋白被磷酸化,層蛋白基質被可逆地分解。層蛋白被認為參與核穩定性、染色質結構和基因表現。層蛋白 A/C 的缺乏可以作為未分化胚胎幹細胞的新標誌,而層蛋白 A/C 的表達則可以作為分化的早期指標 (PMID:16179429)。此基因突變會導致多種疾病:埃默里-德雷福斯肌肉營養不良症、家族性部分脂肪營養不良症、肢帶型肌肉營養不良症、擴張型心肌病變、夏科-馬裡-圖斯病和哈欽森-吉爾福德早衰症。此蛋白經由可變剪接產生4個亞型,分子量分別為74 kDa,65 kDa,70 kDa和64 kDa。此抗體可辨識 4 種 Lamin A/C 亞型。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:1毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為 12 個月。避免凍融循環。避免長時間暴露於光線下。

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Research Areas:訊號傳導;標籤和細胞標記;癌症;細胞生物學;發育生物學;表觀遺傳學和核子訊號;生物化學

Species Reactivity:人類

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Target Synonym:Prelamin-A/C;LMNA;LMN1;Lamin A/C

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Buffer:含0.02%疊氮化鈉、1%保護蛋白和50%甘油的PBS,pH7.4

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Clonality:單複製

Conjugation:Elab Fluor®488

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