庫存單位: E-AB-17889_200μL-ES

DMGDH多株抗體,200 μL

此基因編碼一種參與膽鹼分解代謝的酶,催化二甲基甘氨酸的氧化去甲基化形成肌氨酸。此酵素以單體形式存在於粒線體基質中,並使用黃素腺嘌呤二核苷酸和葉酸作為輔助因子。此基因突變會導致二甲基甘氨酸脫氫酶缺乏症,其特徵是魚腥味、慢性肌肉疲勞以及血清中肌肉形式的肌酸激酶水平升高。可變剪接產生多種轉錄變異。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:2.1 毫克/毫升

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Calculated Molecular Weight:97 千道爾頓

Observed Molecular Weight:參考圖

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:97 千道爾頓

Dilution:寬螢幕 1:500-1:2000

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Features and Capabilities

Application:世界銀行

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Research Areas:代謝;神經科學;訊號傳導

Species Reactivity:人類

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Target Synonym:二甲基甘胺酸脫氫酶;二甲基甘胺酸脫氫酶;粒線體;丹參酮; M2GD;甲基甘胺酸脫氫酶;粒線體

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Clonality:多克隆

Conjugation:未結合

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