庫存單位: E-AB-10155_120μL-ES

COL1A2 多株抗體,120 μL

此基因編碼 I 型膠原蛋白的 pro-alpha2 鏈,其三螺旋包含兩條 alpha1 鏈和一條 alpha2 鏈。 I 型膠原蛋白是一種存在於大多數結締組織中的纖維形成膠原蛋白,在骨骼、角膜、真皮和肌腱中含量豐富。此基因突變與成骨不全症 I-IV 型、埃勒斯-丹洛斯症候群 VIIB 型、隱性埃勒斯-丹洛斯症候群經典型、特發性骨質疏鬆症和非典型馬凡氏症候群有關。然而,與此基因突變相關的症狀往往不如 I 型膠原蛋白 alpha1 鏈(COL1A1)基因突變嚴重,這反映了 alpha2 鏈在基質完整性中的不同作用。已經鑑定出該基因的三種轉錄本,它們是透過使用替代的聚腺苷酸化訊號而產生的。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.1 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:100-1:300

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Application:免疫組織化學

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Research Areas:癌症;訊號傳導;幹細胞

Species Reactivity:人類;小鼠;大鼠

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Target Synonym:Alpha 2 I 型膠原蛋白;Alpha 2 I 型膠原蛋白;Alpha 2 I 型前膠原蛋白;Alpha 2(I) 膠原蛋白;Alpha 2(I) 前膠原蛋白;Alpha-2 I 型膠原蛋白;CO1A2;COL1A2;膠原蛋白 alpha 2(I) 皮膚蛋白;CO1A2;COL1A2;膠原蛋白 alpha 2(I) 皮膚蛋白 Ipha 1A2; 2 鏈;I 型膠原蛋白 alpha 2;OI4;IV 型成骨不全症;I 型前膠原蛋白

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Conjugation:未結合

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