{"product_id":"cbs-polyclonal-antibody-60-μl","title":"CBS 多株抗體，60 μL","description":"\u003cp\u003e\n此基因編碼的蛋白質作為同型四聚體，催化同型半胱胺酸轉化為胱硫醚，這是轉硫途徑的第一步。編碼的蛋白質由腺苷甲硫氨酸變構激活，並使用磷酸吡哆醛作為輔因子。此基因缺陷可導致胱硫醚β合成酶缺乏症（CBSD），進而導致同型胱胺酸尿症。已發現該基因有多種剪接轉錄變異體。\n\u003c\/p\u003e\n\n","brand":"Elabscience","offers":[{"title":"Default Title","offer_id":47120677961952,"sku":"E-AB-14671_60μL-ES","price":171.6,"currency_code":"USD","in_stock":true}],"url":"https:\/\/apac.labcart.com\/zh\/products\/cbs-polyclonal-antibody-60-%ce%bcl","provider":"LabCart Life Science-APAC","version":"1.0","type":"link"}