庫存單位: E-AB-10995_20μL-ES

BCAT1多株抗體,20 μL

此基因編碼酶支鏈氨基酸轉氨酶的細胞質形式。這種酵素能催化支鏈 α-酮酸可逆地轉氨為細胞生長所必需的支鏈 L-胺基酸。兩種不同的臨床疾病被歸因於支鏈胺基酸轉氨酶的缺陷:高纈氨酸血症和高亮氨酸-異亮氨酸血症。由於還存在編碼這種酶的粒線體形式的基因,因此任一基因的突變都可能導致這些疾病。已經描述了替代剪接的轉錄變體。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.4 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:50-1:200

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Application:免疫組織化學

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Research Areas:代謝;訊號傳導

Species Reactivity:人;小鼠

Reactivity:

Target Synonym:BCAT;BCAT(c);Bcat1;BCAT1;BCT1;支鏈胺基酸氨基轉移酶;胞質;支鏈胺基酸轉氨酶 1;胞質;支鏈氨基轉移酶 1;支鏈氨基轉移酶 1;胞質;支鏈胺基酸氨基轉移酶;胞質;DKFZp686E12175; 18;蛋白質 ECA39

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Clonality:多克隆

Conjugation:未結合

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