庫存單位: E-AB-18525_60μL-ES

ATXN3多株抗體,60 μL

馬查多-約瑟夫病,也稱為脊髓小腦性共濟失調-3,是一種體染色體顯性神經系統疾病。此基因編碼的蛋白質在編碼區域含有 (CAG)n 重複序列,從正常的 12-44 擴展到 52-86 是 Machado-Joseph 疾病的原因之一。發病年齡與CAG重複次數呈負相關。已經描述了該基因編碼不同異構體的剪接轉錄變體。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.7 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:50-1:300

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Features and Capabilities

Application:免疫組織化學

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Research Areas:癌症;表觀遺傳學和核子訊號;神經科學

Species Reactivity:人類

Reactivity:

Target Synonym:AT3;共濟失調蛋白3; Ataxin 3 變異體 h;共濟失調蛋白 3 變異 m; Ataxin 3 變異 ref;共濟失調蛋白-3;ATX3; ATX3; ATXN3; EC 3.4.22.;約瑟性神經性腫瘤; ·約瑟夫病;馬查多·約瑟夫病蛋白1; Machado-Joseph 病蛋白 1; Machado-Joseph 病蛋白 1 同源物; MJD; MJD基因; MJD1;橄欖腦橋小腦共濟失調 3; OTTHUMP00000221583;OTTHUMP00000221585; OTTHUMP00000221587;OTTHUMP00000231995; OTTHUMP00000231997; Rsca3;SCA3; SCA3基因;脊髓小腦共濟失調 3 型蛋白

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Clonality:多克隆

Conjugation:未結合

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