庫存單位: E-AB-10990_200μL-ES

ATXN1多株抗體,200 μL

常染色體顯性小腦性共濟失調 (ADCA) 是一組異質性神經退化性疾病,其特徵是小腦、腦幹和脊髓的進行性退化。臨床上,ADCA 分為三類:ADCA I 型至 III 型。 ADCAI 在遺傳上是異質性的,具有五個基因位點,分別指定為脊髓小腦性共濟失調 (SCA) 1、2、3、4 和 6,被分配到五個不同的染色體上。 ADCAII 通常表現為視網膜變性(SCA7),而 ADCAIII 通常被稱為「純」小腦症候群(SCA5),它們很可能是同質性疾病。已克隆了幾種 SCA 基因,並顯示其編碼區含有 CAG 重複序列。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.4 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:50-1:200

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Application:免疫組織化學

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Research Areas:表觀遺傳學和核子訊號;神經科學

Species Reactivity:人類;小鼠;大鼠

Reactivity:

Target Synonym:替代 ataxin1;Ataxin-1;ATX1;ATX1;Atxn1;D6S504E;OTTHUMP00000016065;SCA1;脊髓小腦共濟失調 1 型蛋白

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Conjugation:未結合

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