庫存單位: E-AB-18521_60μL-ES

ASS1多株抗體,60 μL

ASS1是尿素循環中的限速酵素。瓜氨酸血症 I 型是一種體染色體隱性遺傳疾病,由尿素循環酶精氨琥珀酸合成酶 (ASS1) 缺乏所引起。 ASS1 缺乏表現出多種臨床表現,包括患有致命新生兒高氨血症的嚴重受影響患者以及僅有生化表型的無症狀個體。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.5毫克/毫升

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Calculated Molecular Weight:47千道爾頓

Observed Molecular Weight:參考圖

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:47千道爾頓

Dilution:免疫印跡法 1:500-1:2000;免疫組織化學法 1:25-1:100

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Application:免疫組化

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Research Areas:癌症;代謝;訊號傳導

Species Reactivity:人類;小鼠;大鼠

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Target Synonym:精氨酰琥珀酸合成酶1;精氨琥珀酸合成酶;精氨琥珀酸合成酶1;屁股;屁股-1;屁股1;阿薩亞組件;瓜氨酸天冬氨酸連接酶;瓜氨酸-天冬氨酸連接酶;細胞毒性T淋巴細胞1

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Clonality:多克隆

Conjugation:未結合

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