庫存單位: E-AB-10127_120μL-ES

AMACR多株抗體,120 μL

該基因編碼消旋酶。編碼的酵素使 pristanoyl-CoA 和 C27-膽汁醯基輔酶 A 在它們的 (R)- 和 (S)- 立體異構體之間相互轉化。轉化為 (S)-立體異構體對於透過過氧化物酶體 β-氧化降解這些底物是必要的。此基因座編碼的蛋白質定位於粒線體和過氧化物酶體。此基因突變可能與因膽汁酸合成缺陷而導致的成人感覺運動神經病變、色素性視網膜病變和腎上腺脊髓神經病變有關。已經描述了替代剪接的轉錄變體。此基因與上游鄰近的 C1QTNF3(C1q 和腫瘤壞死因子相關蛋白 3)基因之間也存在讀通轉錄。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.1 毫克/毫升

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Calculated Molecular Weight:42kDa

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:42kDa

Dilution:免疫印跡法 1:500-1:2000;免疫組織化學法 1:25-1:100

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Application:免疫組化

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Research Areas:細胞生物學;代謝;訊號傳導

Species Reactivity:人類

Reactivity:

Target Synonym:2 甲基醯基輔酶 A 消旋酶;2-甲基醯基輔酶 A 消旋酶;α 甲基醯基輔酶 A 消旋酶;α-甲基醯基輔酶 A 消旋酶;Amacr;AMACR;AMACRD;CBAS4;EC 5.1.99.4;Macr1;RACE;RMr1;RACE;RMr1;RACE;

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Clonality:多克隆

Conjugation:未結合

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