{"product_id":"aldh6a1-polyclonal-antibody-20-μl","title":"ALDH6A1 多株抗體，20 μL","description":"\u003cp\u003e \n此蛋白質屬於醛脫氫酶蛋白質家族。這種酵素在纈氨酸和嘧啶分解代謝途徑中發揮作用。此基因的產物，粒線體甲基丙二酸半醛脫氫酶，催化丙二酸和甲基丙二酸半醛不可逆氧化脫羧為乙醯輔酶 A 和丙醯輔酶 A。甲基丙二酸半醛脫氫酶缺乏症的特徵是尿液有機酸中β-丙氨酸、3-羥基丙酸以及3-氨基和3-羥基異丁酸的兩種異構體升高。\n\u003c\/p\u003e\n\n","brand":"Elabscience","offers":[{"title":"Default Title","offer_id":47121471209696,"sku":"E-AB-10769_20μL-ES","price":87.6,"currency_code":"USD","in_stock":true}],"url":"https:\/\/apac.labcart.com\/zh\/products\/aldh6a1-polyclonal-antibody-20-%ce%bcl","provider":"LabCart Life Science-APAC","version":"1.0","type":"link"}