庫存單位: E-AB-10769_120μL-ES

ALDH6A1 多株抗體,120 μL

此蛋白質屬於醛脫氫酶蛋白質家族。這種酵素在纈氨酸和嘧啶分解代謝途徑中發揮作用。此基因的產物,粒線體甲基丙二酸半醛脫氫酶,催化丙二酸和甲基丙二酸半醛不可逆氧化脫羧為乙醯輔酶 A 和丙醯輔酶 A。甲基丙二酸半醛脫氫酶缺乏症的特徵是尿液有機酸中β-丙氨酸、3-羥基丙酸以及3-氨基和3-羥基異丁酸的兩種異構體升高。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.4 毫克/毫升

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Calculated Molecular Weight:58kDa

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:58kDa

Dilution:免疫印跡法 1:500-1:2000

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Application:免疫組化

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Research Areas:癌症;代謝;訊號傳導

Species Reactivity:人類;小鼠;大鼠

Reactivity:

Target Synonym:1110038I05Rik;AI314632;醛脫氫酶 6 家族成員 A1;醛脫氫酶家族 6 成員 A1;醛脫氫酶家族 6;亞家族 A1;ALDH6A1;丙二酸半醛脫氫酶;丙二酸半醛脫氫酶 [CKHMGx32]; ;MGC40271;粒線體醯化甲基丙二酸半醛脫氫酶;粒線體;MMSA;MMSADHA;MMSDH

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Clonality:多克隆

Conjugation:未結合

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