庫存單位: E-AB-12706_200μL-ES

AGXT多株抗體,200 μL

絲氨酸-丙酮酸氨基轉移酶是人類的一種酶,由 AGXT 基因編碼。此基因僅在肝臟中表達,編碼的蛋白質主要位於過氧化物酶體,參與乙醛酸的解毒。該基因的某些突變會改變亞細胞靶向,與 I 型原發性高草酸尿症有關。 AGXT 缺陷是原發性高草酸尿症 1 型 (HP1) 的病因,也稱為原發性高草酸尿症 I 型 (PH1) 和草酸沉著症 I。 HP1 是一種罕見的體染色體隱性遺傳性乙醛酸代謝缺陷,其特徵是草酸和乙醇酸排泄增加,以及不溶性草酸鈣在腎臟和泌尿道中逐漸積聚。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.6 毫克/毫升

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Calculated Molecular Weight:43kDa

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:43kDa

Dilution:寬螢幕 1:500-1:2000

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Features and Capabilities

Application:世界銀行

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Research Areas:癌症;代謝;訊號傳導

Species Reactivity:人類;小鼠;大鼠

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Target Synonym:AGT;AGT1;Agxt;AGXT1;丙氨酸乙醛酸氨基轉移酶;丙氨酸乙醛酸氨基轉移酶3;丙氨酸-乙醛酸氨基轉移酶;EC 2.6.1.44;EC 2.6.1.51;肝過氧化物酶體丙氨酸乙醛酸氨基轉移酶;肝過氧化物酶胺丙氨酸1751; ;絲胺酸-丙酮酸氨基轉移酶;絲胺酸-丙酮酸氨基轉移酶;粒線體;絲胺酸:丙酮酸氨基轉移酶;SPAT;SPT;SPYA;TLH6

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Clonality:多克隆

Conjugation:未結合

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