庫存單位: E-BC-K821-M_96T-ES

α-葡萄糖苷酶(α-GC)活性測定試劑盒,96T

α-葡萄糖苷酶(α-GC)又稱為α-D-葡萄糖苷水解酶,在自然界分佈廣泛,種類繁多,性質各異,幾乎存在於所有生物體中。在動物、植物和微生物的碳水化合物代謝中具有重要的生理功能。如果α-GC缺乏,則導致嚴重的肝醣代謝障礙,肝醣蓄積過多,可引起龐帕症(一種體染色體隱性遺傳的肝醣累積病,又稱為肝醣積累II型)。人體組織中長期α-GC活性較低,可造成肌肉纖維破壞,肌肉萎縮。 本試劑盒的檢測原理為α-葡萄糖苷酶催化底物反應生成的顯色物質在400nm處有最大吸收,測定其在400nm處的OD值即可反映α-GC的酵素活性。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Sensitivity:0.35單位/公升

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Shelf Life:12個月

Storage:本品在-20℃避光條件下可保存12個月。

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Detection Type:比色法

Detection Range: 0.35-33.43 單位/公升

Research Areas:糖解作用和脂質代謝

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Target Synonym:α-葡萄糖苷酶

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Result Type:酵素活性

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Assay Time:50 分鐘

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Detection Instrument :微孔板讀數儀

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