庫存單位: E-AB-10671_200μL-ES

pVHL 多株抗體, 200 μL

馮希佩爾-林道綜合症(VHL)是一種顯性遺傳的家族性癌症綜合徵,易患多種惡性和良性腫瘤。此基因的種系突變是 VHL 症候群家族遺傳的基礎。此基因編碼的蛋白質是包含 elongin B、elongin C 和 cullin-2 的蛋白質複合物的組成部分,並具有泛素連接酶 E3 活性。此蛋白質參與缺氧誘導因子 (HIF) 的泛素化和降解,HIF 是一種在氧調節基因表現中起核心作用的轉錄因子。據報道,RNA 聚合酶 II 亞基 POLR2G/RPB7 也是此蛋白質的標靶。已經觀察到編碼不同異構體的剪接轉錄變體。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:0.4 毫克/毫升

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Dilution:免疫組化 1:50-1:200

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Application:免疫組織化學

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Research Areas:癌症;細胞生物學;表觀遺傳學和核信號;代謝

Species Reactivity:人類

Reactivity:

Target Synonym:延伸蛋白結合蛋白;G7 蛋白;HRCA 1;HRCA1;蛋白 G7;pVHL;RCA 1;RCA1;VHL 1;VHL;VHL;VHL1;VHLH;馮·希佩爾·林道病腫瘤抑制因子;馮·希佩爾·林道綜合徵;馮希·佩爾·林道腫瘤抑制因子;馮·林道腫瘤抑制因子;馮·林道綜合徵;馮·希道蛋白連接因子;

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Buffer:含0.05%疊氮化鈉和50%甘油的PBS,PH7.4

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Clonality:多克隆

Conjugation:未結合

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