庫存單位: E-AB-52930_120μL-ES

PDHA1多株抗體,120 μL

PDHA1(丙酮酸脫氫酶 E1 組分亞基 α,體細胞形式,粒線體)也稱為 PHE1A。它是丙酮酸脫氫酶複合物的 3 種酶之一,該複合物是一種核編碼的線粒體基質多酶複合物,透過催化丙酮酸不可逆轉化為乙醯輔酶 A,提供糖酵解和三羧酸 (TCA) 循環之間的主要聯繫。它具有 4 種由可變剪接產生的同工型。 PDHA1 缺陷是導致丙酮酸脫氫酶 E1-alpha 缺乏症 (PDHAD) 和 X 連鎖 Leigh 症候群 (X-LS) 的原因。

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Product Specification

Basic Information

Brands:Elabscience

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Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Calculated Molecular Weight:43千道爾頓

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:43千道爾頓

Dilution:白血球介素 1:1000-1:5000;免疫組織化學 1:50-1:300

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Application:免疫組化

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Research Areas:癌症;代謝;訊號傳導

Species Reactivity:人類;小鼠;大鼠

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Target Synonym:ODPA;PDH;PDHA;PDHA1;PDHCE1A;PDHE1 A 型 I;PDHE1-A 類型 I;PHE1A;丙酮酸脫氫酶(硫辛酰胺)α1;丙酮酸脫氫酶複合物;E1 α多肽 1;丙酮酸脫氫酶 E1 α;丙酮酸脫氫酶複合物;E1 α多肽 1;丙酮酸脫氫酶 E1 α;丙酮酸脫氫酶複合物;E1 α多肽 1;丙酮酸脫氫酶 E1 α;丙酮酸脫氫酶複合物;E1 α多肽 1;丙酮酸脫氫酶 E1 α;丙酮酸脫氫酶複合物;

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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