庫存單位: E-AB-70211_60μL-ES

NPHS1 多克隆抗體,60 μL

此基因編碼免疫球蛋白家族的細胞黏附分子成員,在腎臟的腎小球濾過屏障中發揮作用。此基因主要在腎臟組織中表達,蛋白質是在腎小球足細胞裂孔隔膜中發現的1型跨膜蛋白。狹縫隔膜被認為起著超濾器的作用,排除尿液形成過程中的白蛋白和其他血漿大分子。此基因突變會導致芬蘭型先天性腎病變 1,其特徵是嚴重蛋白尿和裂孔膈和足突的消失。在蛋白質印跡法中,針對重組人類腎小球蛋白的兩個末端胞外 Ig 結構域產生的腎小球蛋白抗體可辨識人類腎小球裂解物中的 180 kDa 蛋白質和轉染的 COS-7 細胞裂解物中的 150 kDa 蛋白質。

定價
$192.00 USD
售價
$192.00 USD
定價
2-4週
Hassle-Free Warranty
Safe & Secure Payment
Livetime Tech Support
  • Specification
  • Downloads
  • Reviews
$192.00
ADD TO CART
ADD TO CART

Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

Warranty:

Safety Performance:

Protection Class:

Sterile Status:

Reconstitution:

Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

Battery:

Battery Service Life:

Component:

Technical Specifications

Capacity:

Concentration:1.3 毫克/毫升

Dimension [D×W×H]:

Diameter:

Length:

Width:

High:

Volume:

Volume Range:

Speed:

Speed Range:

Max.Speed:

Max. RCF:

Temperature Range:

Operating Temperature Range:

Permissible Ambient Temperature :

Permissible Relative Humidity:

Input voltage:

Power Requirements:

Voltage/Frequency:

Sensitivity:

Specificity:

Precision:

Speed Accuracy:

Volume Accuracy:

Particle Size:

Pore Size:

Binding Capacity:

Calculated Molecular Weight:

Observed Molecular Weight:

Purity:

Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

Random Error:

Acceleration/Braking time:

Aspiration Speed:

Calculated Molecular Weight:

Dilution:免疫組化 1:1000-1:2000

Driving Motor DC motor:

Em:

Ex:

Endotoxin:

Flow rate [liquid]:

Features and Capabilities

Application:免疫組織化學

Detection Target:

Detection Type:

Detection Range:

Research Areas:癌症;訊號傳導

Species Reactivity:老鼠

Reactivity:

Target Synonym:CNF;Nephrin;先天性芬蘭型腎病變 1;先天性腎病變 1;芬蘭型 (nephrin);NPHN;NPHN;NPHS 1;Nphs1;腎小球特異性細胞黏附受體;腎小球特異性細胞黏附受體

Test Principle:

Quantitative/Qualitative :

Result Type:

Materials :

Assay Time:

Autoclave component:

Available Rotor Adapters:

Binding Capacity:

Bio-activity:

Bottom Shape:

Bottom Type:

Buffer:含0.02%疊氮化鈉、1%保護蛋白和50%甘油的PBS,pH7.4

Cap Color:

Clonality:多克隆

Conjugation:未結合

Coupled Ligand:

Cover Type:

Detection Instrument :

Dispensing Speed:

Display:

Form:

Formulation:

Graduation:

Growth Area:

Download File