庫存單位: E-AB-17786_120μL-ES

CECR5多株抗體,120 μL

腺苷脫氨酶是一種存在於大多數組織中的酶,主要以單體形式存在,儘管在某些組織中它與腺苷脫氨酶結合蛋白有關。腺苷脫氨酶降解細胞外腺苷,對淋巴球有毒性。已經發現了一個與腺苷脫氨酶具有序列相似性的新型生長因子家族。貓眼症候群關鍵區域蛋白 (CECR) 家族包括 CECR1、CEC​​R2、CECR3、CECR4、CECR5、CECR6、CECR7、CECR8 和 CECR9。編碼 CECR 蛋白的基因是貓眼症候群 (CES) 的候選基因,這是與 22q11.2 的 2 Mb 區域重複有關的發育障礙。 CES 的特徵是虹膜缺損和肛門閉鎖併發瘻管,瞼​​裂向下傾斜,耳前贅生物和/或小窩,經常發生心臟和腎臟畸形,以及正常或接近正常的智力發育。 CECR家族成員表達廣泛。具體來說,CECR1在成人心臟、肺臟、淋巴母細胞和胎盤中表達最高。 CECR2 也參與神經管形成和染色質重塑。 CECR2 基因突變會導致神經管缺陷。

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Product Specification

Basic Information

Brands:Elabscience

Model Number:

Place of Origin:中國

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Shipping:產品隨附冰袋,收到後,請立即在建議的溫度下存放。

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Concentration:1.3 毫克/毫升

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Calculated Molecular Weight:46千道爾頓

Observed Molecular Weight:參考圖

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Shelf Life:12個月

Storage:儲存於-20°C,有效期限為12個月。避免凍融循環。

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Calculated Molecular Weight:46千道爾頓

Dilution:寬螢幕 1:500-1:2000

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Features and Capabilities

Application:世界銀行

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Research Areas:細胞生物學

Species Reactivity:人類

Reactivity:

Target Synonym:A930002G03里克;貓眼症候群染色體區域;候選人5;貓眼症候群染色體區域;候選5同源物;貓眼症候群關鍵區域蛋白5;鈰5;CECR5;MGC25951;OTTMUSP00000025905

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Buffer:含 0.05% NaN3 和 40% 甘油的 PBS,pH7.4

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Clonality:多克隆

Conjugation:未結合

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